Fibrous Dysplasia of the Clivus
نویسندگان
چکیده
منابع مشابه
Monostotic fibrous dysplasia of the clivus: imaging findings.
Fibrous dysplasia (FD) is an uncommon benign disorder of unknown etiology. It most likely represents a disorder of normal bone development. The disease can involve any bone in the body. In the head and neck, the skull and facial bones are involved in 10-25% of cases of monostotic FD. Involvement of the clivus in monostotic FD is extremely unusual, and has rarely been reported previously. The di...
متن کاملFibrous dysplasia of the clivus, a case report
Introduction Fibrous dysplasia (FD) of the clivus, first described by Lichtenstein in 1938, is a very rare developmental, non-hereditary disorder caused by abnormal proliferation and maturation of fibroblasts resulting in replacement of mature bone by weak and immature bone.
متن کاملCraniofacial Fibrous Dysplasia
Fibrous dysplasia (FD) is an osseous growth dis-order, producing immature bone and characte-rized by the replacement of normal bone with fibro-osseous connective tissue. It is a bone dys-plasia that has the potential to cause significant cosmetic and functional disturbances, particularly in the craniofacial skeleton. Cra-niofacial fibrous dysplasia is one of the three types of polyostotic fibro...
متن کاملCraniofacial Fibrous Dysplasia of Zygomaticomaxillary Complex
Fibrous dysplasia is a benign bone disease first described by Lichtenstein in 1938. It is characterized by progressive replacement of normal bone with fibro-osseous connective tissue. When the disease involves craniofacial skeleton, it results in significant disfigurement and other functional problems. This paper reports a case of large craniofacial fibrous dysplasia involving zygomaticomaxilla...
متن کاملThe nature of fibrous dysplasia
Fibrous dysplasia has been regarded as a developmental skeletal disorder characterized by replacement of normal bone with benign cellular fibrous connective tissue. It has now become evident that fibrous dysplasia is a genetic disease caused by somatic activating mutation of the Gsalpha subunit of G protein-coupled receptor resulting in upregulation of cAMP. This leads to defects in differentia...
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ژورنال
عنوان ژورنال: Journal of Korean Neurosurgical Society
سال: 2010
ISSN: 2005-3711
DOI: 10.3340/jkns.2010.48.5.441